{{Infobox medical condition (new)
| name = 埃勒斯-當洛斯症候群
| image = Ehlers-Danlos syndrome4.jpg
| caption = 松皮症患者 (individual with EDS displaying skin hyperelasticity)
| field = 醫學遺傳學 (medical genetic)
| pronounce =
| symptoms = 过于灵活的关节 (overly flexible joints), 有弹性的皮肤(stretchy skin), 不正常疤痕的形成 (abnormal scar formation)
| complications = 主动脉夹层 (aortic dissection), 脫臼 (joint dislocations), 骨关节炎 (osteoarthritis)
| duration = 长期(long term)
| causes = 遗传
| medication =
| prognosis = 取决于类型 (depends on the type)(I型到X型)。1997年,研究人員在此基础上提出了一种较为簡單的分類方式(Villefranche分型),將它的主要類型分成六種,即:关节过度活动型(Hypermobility type,EDS III型)、经典型(Classical type,EDS I/II型)、血管型(Vascular type,EDS IV型)、脊柱侧后凸型(Kyphoscoliosis type,EDS VI型)、关节松弛型(Arthrochalasia type,EDS VIIA/VIIB型)和皮肤脆裂型(Dermatosparaxis type,EDS VIIC型)。
2017年新修订的EDS分类则将其分为13种亚型,包括:
经典型EDS(Classical EDS)
经典样EDS(Classical-like EDS)
心脏-瓣膜型EDS(Cardiac-valvular EDS)
血管型EDS(Vascular EDS)
关节过度活动型EDS(Hypermobile EDS)
关节松弛型EDS(Arthrochalasia EDS)
皮肤脆裂型EDS(Dermatosparaxis EDS)
脊柱侧后凸型EDS(Kyphoscoliotic EDS)
脆性角膜综合征(Brittle Cornea syndrome)
脊椎变异型EDS(Spondylodysplastic EDS)
肌肉挛缩型EDS(Musculocontractural EDS)
肌病型EDS(Myopathic EDS)
牙周病型EDS(Periodontal EDS)
著名患者
註釋
外部連結
*
- [http://www.ncbi.nlm.nih.gov/books/NBK1244/ Ehlers–Danlos Syndrome, Classic Type. Includes: Ehlers–Danlos Syndrome Type I, Ehlers–Danlos Syndrome Type II]
- [https://web.archive.org/web/20170629012136/http://www.orthop.washington.edu/?q=patient-care%2Farticles%2Farthritis%2Fehlers-danlos-syndrome.html University of Washington Medicine, Orthopaedics and Sports Medicine] Multi-page explanation of EDS, including symptoms, genetics, diagnosis, and treatment
- [http://www.ncbi.nlm.nih.gov/bookshelf/br.fcgi?book=gene&part=eds3 National Institute of Health on Hypermobility EDS]
- [http://www.ncbi.nlm.nih.gov/books/NBK1494/ GeneReviews/NCBI/NIH/UW entry on Ehlers–Danlos Syndrome Type IV]
*
- [http://arquivo.pt/wayback/20160525070446/http://www.ednf.org/ Ehlers–Danlos National Foundation]
- [http://hypermobile.co.uk/index.php?option=com_content&view=article&id=157&Itemid=37 Hypermobile – A blog about Ehlers Danlos Syndrome] The lack of clinical distinction between the hypermobility type of Ehlers–Danlos syndrome and the joint hypermobility syndrome (a.k.a. hypermobility syndrome)
- [http://www.ncbi.nlm.nih.gov/pubmed/22786715 Management of pain and fatigue in the joint hypermobility syndrome (a.k.a. Ehlers–Danlos syndrome, hypermobility type): principles and proposal for a multidisciplinary approach]
- [https://web.archive.org/web/20150415011744/http://www.orphananesthesia.eu/en/rare-diseases/published-guidelines/cat_view/61-rare-diseases/60-published-guidelines/89-ehlersdanlos-syndrome.html?limit=5&limitstart=0&order=hits&dir=ASC Anesthesia for EDS patients - Guidelines at orphananesthesia.eu]
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