GM2 (神经节苷脂)

{{Chembox
| Name = GM2
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| verifiedrevid = 458296360
| ImageFile = GM2 ganglioside.png
| ImageSize = 250px
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| IUPACName = (2S,3R,4E)-3-Hydroxy-2-octadecanamidooctadec-4-en-1-yl (5-acetamido-3,5-dideoxy-D-glycero-α-D-galacto-non-2-ulopyranosylonic acid)-(2→3)-[2-acetamido-2-deoxy-β-D-galactopyranosyl-(1→4)]-β-D-galactopyranosyl-(1→4)-β-D-glucopyranoside
| SystematicName = (2S,4S,5R,6R)-5-Acetamido-2-{[(2R,3S,4R,5R,6S)-3-{[(2S,3R,4R,5R,6R)-3-acetamido-4,5-dihydroxy-6-(hydroxymethyl)oxan-2-yl]oxy}-6-{[(2R,3S,4R,5R,6R)-4,5-dihydroxy-2-(hydroxymethyl)-6-{[(2S,3R,4E)-3-hydroxy-2-octadecanamidooctadec-4-en-1-yl]oxy}oxan-3-yl]oxy}-5-hydroxy-2-(hydroxymethyl)oxan-4-yl]oxy}-4-hydroxy-6-[(1R,2R)-1,2,3-trihydroxypropyl]oxane-2-carboxylate
| OtherNames = Ganglioside GM2; Tay–Sachs ganglioside;
β-D-GalNAc-(1→4)-[α-Neu5Ac-(2→3)]-β-D-Gal-(1→4)-β-D-Glc-(1↔1)-N-octadecanoylsphingosine
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在有机化学中,GM2是神经节苷脂的一种。G指神经节苷脂,M代表单唾液酸(因为它有一个唾液酸),2指它是第二种被发现的单唾液酸神经节苷脂。它与GM2神经节苷脂沉积症(例如泰-萨克斯病)有关。

参见

  • GM2A

附加图集
Image:Sphingolipidoses.svg|鞘脂沉积症
Image:Structure of GM1, GM2, GM3.png|GM1、GM2、GM3神经节苷脂的结构

参考资料
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